Index

Allelic Variants

 

Wild DNA Sequence (with mutations highlighted)-

ORIGIN     

        1 gtcggcgagg agggtccggc cggagttgaa ggattgaact ttccggctca gtcgcggcgt

       61 ctgcctggtc ctcagcagtg cagccccggc gcggagcagg gagcctcggc ccgcgcccgg

      121 cgccctcgcc ctcgccctcg acccgcagcc atggtgcccg gggtgcccgg cgcggtcctg

      181 accctctgcc tctggctggc ggcctccagc ggctgcctgg cggccggccc cggcgcggct

      241 gctgcgcggc ggctggacga gtcgctgtct gccgggagcg tccagcgcgc tcgctgcgcc

      301 tccaggtgcc tgagcctgca gatcactcgc atctccgcct tcttccagca cttccagaac

      361 aatggttccc tggtttggtg ccagaatcac aagcaatgtt ctaagtgcct ggagccctgc

      421 aaggaatcag gggacctgag gaaacaccag tgccaaagct tttgtgagcc tctcttcccc

      481 aagaagagct acgaatgctt gaccagctgt gagttcctca aatacatcct gttggtgaag

      541 cagggggact gtccggctcc tgagaaagcc agtggatttg cggccgcctg tgttgaaagc

      601 tgcgaagttg acaatgagtg ctctggggtg aagaaatgtt gttcgaatgg gtgtggacac

      661 acctgtcaag tacccaagac tctgtacaaa ggtgtccccc tgaagcccag gaaagagtta

      721 cgatttacag aactgcagtc tggacagctg gaggttaagt ggtcctcgaa cttgaatatt

      781 tctattgagc ctgtgatcta tgtggtacaa agaagatgga attatggaat ccctcctagc

      841 gaagatgacg ccactcactg gcagacagtg gcccagacca cagacgagcg agttcaactg

      901 actgacataa gacccagccg atggtaccag tttcgagtgg ctgctgtgaa tgtgcatgga

      961 actcgaggct tcactgcccc cagcaaacac ttccgttctt ccaaagatcc atctgcccca

     1021 ccagcaccgg ctaacctccg gctggccaac tccaccgtca acagtgatgg gagtgtgacc

     1081 gtcactatag tttgggatct ccccgaggag ccggacatcc ctgtgcatca ttacaaggtc

     1141 ttttggagct ggatggtcag cagtaagtct cttgtcccaa caaagaagaa gcggagaaag

     1201 actacggatg ggtttcaaaa ttctgtgatc ctggagaaac tccagccaga ctgtgactat

     1261 gttgtggaat tgcaagccat aacgtactgg ggacagacac ggctgaagag tgcaaaggtg

     1321 tcccttcact tcacatcgac acatgcaacc aacaacaaag aacagcttgt gaaaactaga

     1381 aaaggtggaa ttcaaacaca actccctttt caaagacgac gacccactcg cccgctggaa

     1441 gtcggagctc ccttctatca ggatggccaa ctgcaagtta aagtctactg gaagaagaca

     1501 gaagatccca ctgtcaaccg atatcatgtg cggtggtttc ctgaagcgtg tgcccacaac

     1561 agaacaaccg gatcagaggc atcatctggc atgacccacg aaaattacat aattcttcaa

     1621 gatctgtcat tttcctgcaa gtataaggtg actgtccaac caatacggcc aaaaagtcac

     1681 tccaaggcag aagctgtttt cttcactact ccaccatgct ctgctcttaa ggggaagagc

     1741 cacaagcctg ttggctgcct gggcgaagca ggtcatgttc tttctaaggt gctagctaag

     1801 cctgagaacc tttctgcttc attcatcgtc caggatgtga acatcaccgg tcacttttct

     1861 tggaagatgg ccaaggccaa tctctatcag cccatgactg ggtttcaagt gacttgggct

     1921 gaggtcacta cggaaagcag acagaacagc ctacccaaca gcattatttc acagtcccag

     1981 atcctgcctt ccgatcatta tgtcctaaca gtgcccaatc tgagaccatc tactctttac

     2041 cgactggaag tgcaagtgct gaccccagga ggggaggggc cggccaccat caagacgttc

     2101 cggacgccgg agctcccacc ctcttcagca cacagatctc atcttaagca tcgtcatcca

     2161 catcattaca agccttctcc agaaagatac taaactgttc aaaaagattt tgtgaaattg

     2221 cacagatgtg taagcttgtt gaacttcggc cacgagacat gcacacttcc agaggcagtg

     2281 ggaactgctc agaggcccgg actctcctat gtgactttag tgcaggaaga acttctgtca

     2341 atcatggacg catctggaga caagtgagaa acagtagatt ggtgaagaca gacaccagtt

     2401 ccctacaagc atggagaaaa tgaagaatag gcctgtttaa tgctaaattt tgttttcatg

     2461 tatggtgtcg ctcatttcta ttgaattaca acagaactca gttttccctg aatttggagc

     2521 accaaactcc gccccaaaaa ggagagtaac aaatacacaa ttcacacata acactaagcg

     2581 taaatctaat caataaaata tatttttgac taaattattg attcgatatg aaaaatcaac

     2641 taagattaca cagctttgtt tttttgaatc tttcctaaga tcatttttat cctaggtgat

     2701 ttttaaatga aaatgtgtaa tctaaaatat accagcgaat ttaaatctaa aaatgctcct

     2761 actttaagta ccttgtgctg ctctttatgc aaaggtaaat caaagttccc tctataaatt

     2821 atgatttaca aaagacaccc aagccagagg aactcaatga aataagctgc taatcagatt

     2881 ttaccttgga gaaatgaaaa ttatttcttg gggatgcctt ttaatatttg atcctattat

     2941 gtgagagatt ttcctgatat gttatcttat ttatattttc ccttattttc ctcaatgcag

     3001 ataatagctt ttggtgcact tttgtttcac catctgaaaa ttcacaaaac ttcttgcttc

     3061 aaatgaaaaa atcccaacta ttgagcatgt ttaaatcttt gcagagattt gccttttctt

     3121 aatcaaagaa aggtctttgt gtgctagaat attattggta atgttttaaa aattcctttg

     3181 attgatagag aaggacagtt atttgcattt aattcaccca tatgctttca aatctagtat

     3241 atcttacttt ttggaaatgt tttatgctac aaattagtgc cttgtagcat gaacttaagt

     3301 caaaacgtgt tatcaatata gagtgttgca gtgtatattg taacaaccta aaacgcagag

     3361 aagtttaatt taatactgtt ttttttcttg aaggaatact cacatacatg gtttgaaatg

     3421 tgcatagata tgcatgtcta tataattata aatgcatgtg tatatatatg caaatatatg

     3481 tacatataca tgtatataca cacagacaca tgcatataca tgaatatacc ttgagcatga

     3541 atccctggag aaatcgtttt cgtagctcac caatggtgag taaagataca gctcttttaa

     3601 aggtcataag gataatatat tttccccatc aatgctgatt ctgagaaaag agcaatttat

     3661 caaaattaaa cactgtaaaa gaaaggtgtc catatgtctt tacctaccta agtaaaacag

     3721 gaagaaaatc agtaacatta tccttaggtt ttgacaatgg tacttgcttc ttgttgtttt

     3781 attgtttcct gaattcatgc agatgcctgg ccattcctgg gaagagtgga taactcagaa

     3841 gtcactgtac tccacagagc ctcactgcag tgtctaaagg tagatgcaaa ttaaaatgca

     3901 gggaaaataa cttttctgat gttgatgcat gtctttggga aacacattta taaacatgga

     3961 tacctgataa tagatattga aacccatttc ctgtgtgtta aaatatttaa aaagtggata

     4021 ttccaggaat gttttgcagc tttgtacaag taacataaat tggacacctc agaatgaaag

     4081 ttcatgttgg ttctgaatgg ttcactgcag ctcctgtcac aagctgggat ggatttatca

     4141 cattgagtta tgaaattacc tggttctaag aatttttgag tggcaaaaat agaaaacaat

     4201 cttcatttga aaacatccct aagcttgaat aaatggatac catagatagc ttctcttttt

     4261 tattctggtg tcattaccag catctgaatt tcaagttctt aaaatttcaa aaattaaaat

     4321 ttttcattat tagctatcca tttatctttt acatgaactt gtcatgaaca aattcaaatg

     4381 tttatgccag caaatttttg tactgttgca tagttaaaaa tgctgggagt ctctgcatag

     4441 atacaaaata ttattaaatt attacataaa tttaatttta taaaatttaa tcatgcttct

     4501 tttgtctggg taatagacat tggacagata tttttagttc agatggtgat tctgaagctt

     4561 acatctccct taaaaaaatc taaagcagct cttatgggct tctaatttta atataaataa

     4621 ataatttaaa ttttattggt gttattggaa gaaaaatgct attaatgggc taataaaaaa

     4681 catgtgtttc tcttatggat tttaataagc tccagtatta ttcaaatgat caaaaatata

     4741 gttataattt tttgaatttt aaaaatgtga ttgctctaat aaagaataaa atctatgctt

     4801 tttaacaaac atagttttgg tgcctaattc tgtaatatgt tttattgaaa ttagattcat

     4861 ttctctaatg tgagaaaaat atatccagta atagtattga ctgtttaaaa aattgagctc

     4921 atcaaaaata ttgtcatcaa atacaggtgg ttaatctgac atacattgca gttacatgca

     4981 ttatttttat ttacaacatt tgctccttaa tgatgaattt atctgtgtta ccctgttttt

     5041 ctacctggaa ctccatagaa tgatgtttgc aaaccaacat gtgctctttt cagtcattca

     5101 ctgttttaat atgacatggt agagaagata aggtttatgg caggtaattt tttgtaatgt

     5161 gtattaaacg aagttcaaag attagaaata catctgtgtc ctgaaaacct tagatacata

     5221 gccgactgta tacagaggtt catctcaacc tcaacactat tgacttttgg ggctggatag

     5281 ttctctgttg tgggggtttg tcttgtgcac tgtaggtttt tagtagcatc cacactttct

     5341 cctcaccaga tgccagttgc accctccccc aagttgagac aaccaaaaat gtctccagat

     5401 attgccagct accccttgag ggatggtacc tctggttgag aaccattgct agagaatgat

     5461 ctttactgaa tttgcccttt ataagaaacc cagtgaattt ctagagcaag tcccaaaaac

     5521 taagggacag ctaagaagtt attatggttg acttcaaagg cctaaactgt gttttttatg

     5581 tccactaaac aacttgatta aaagacggaa ttttgactcg tgtctgtatc atacaagtac

     5641 aaatactaat tttgccctat gtatccgtaa atgtcatttg tgattttgac ttatttattt

     5701 aatgcccttt cttatgccgt gggttttcaa gtttactcat ttctatggtt gcaaataact

     5761 ctaaaactta ttatataaac tttcatatta taggcagaac acaatggcta aatatctgtt

     5821 gcatgtactt taaagtttat tataaaatat aaacagatat ataaagatgt tgactcttac

     5881 ctgtgatttt gcatggtcag actcggtgtc aggtacggag aggattctca tgactgtctt

     5941 acctctactg aatattctag tgagttatat gatttacgga gtgattaaca gaggtctata

     6001 taaagttact tttccccttt acttaattat attgtagtgt gcagataaca aaactgctac

     6061 cttctcatcc aagtggtctg tagaattcat gtcccttaca gtggtcattt aaagtcaata

     6121 tttatttatg tatgtaataa aaaaagttgg atttttgtgt atgtctgtca cattatttag

     6181 agagaagtaa tcttgtaaaa atgttttgta aaaaacaaaa aagtattgta aatagtcttg

     6241 atattctgtg actcattatt ttcatgttag agtttgtaca tactggttca ataataaagt

     6301 atccttaaac caga

Then, through transcription, and, later, translation, the following wild protein sequence succeeds the previous wild DNA sequence.

Wild Protein Sequence (with mutations highlighted)-

ORIGIN     

        1   mvpgvpgavl tlclwlaass gclaagpgaa aarrldesls agsvqrarca srclslqitr

      61 isaffqhfqn ngslvwcqnh kqcskclepc kesgdlrkhq cqsfceplfp kksyecltsc

      121 eflkyillvk qgdcpapeka sgfaaacves cevdnecsgv kkccsngcgh tcqvpktlyk

      181 gvplkprkel rftelqsgql evkwsskfni siepviyvvq rrwnygihps eddathwqtv

      241 aqttdervql tdirpsrwyq frvaavnvhg trgftapskh frsskdpsap papanlrlan

      301 stvnsdgsvt vtivwdlpee pdipvhhykv fwswmvssks lvptkkkrrk ttdgfqnsvi

      361 leklqpdcdy vvelqaityw gqtrlksakv slhftsthat nnkeqlvktr kggiqtqlpf

      421 qrrrptrple vgapfyqdgq lqvkvywkkt edptvnryhv rwfpeacahn rttgseassg

      481 mthenyiilq dlsfsckykv tvqpirpksh skaeavfftt ppcsalkgks hkpigclgea

      541 ghvlskvlak penlsasfiv qdvnitghfs wkmakanlyq pmtgfqvtwa evttesrqns

      601 lpnsiisqsq ilpsdhyvlt vpnlrpstly rlevqvltpg gegpatiktf rtpelppssa

      661 hrshlkhrhp hhykpspery

Allelic Variants

 

Allelic Variants

DNA Change

Amino Acid (Protein Change)

1.

Guanine to Adenine transition change at base pair 711

Tryptophan to a premature terminal codon at 237

2.

Cytosine to thymine transition change at base pair 771

Arginine to a a premature terminal codon at 257

3.

Guanine to Adenine transition change at base pair 774

Tryptophan to a premature terminal codon at 258

4.

Deletion of one of 'Cytosine' nucleotides at base pair 831 (previously a cytosine-cytosine-cytosine, and now, a cytosine-cytosine), resulting in a frameshift

Deletion of Proline, leading  to a premature terminal codon at 277

 

 http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=308700      OMIM

http://www.ncbi.nlm.nih.gov/bookshelf/br.fcgi?book=gene&part=kms  OMIM